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Polisitemia Vera
Oleh:
Hanna Damayanti10.2012.337
C6
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Hasil Pemeriksaan Fisik
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Pemeriksaan Penunjang
1. Laboratorium Hemoglo(in: 1 g/
rom(osit 550.000m/ /eukosit 2.000 selmm3
4ritosit 6.000.000=/
Hematokrit 5
"etikulosit 2+5.
Darah te!i normositik normokrom+ i *ount1163151
2. Sitogenetik
3. Sumsum tulang
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Gejala klinis
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Working diagnosis
8 Polisitemia Vera> !enyakit kelainan !aa sistem mielo!rolierati→unsur hemo!oetik sumsum tulang;→ se(agian!o!ulasi eritrosit (erasal ari satu klon sel inuk
arah yang a(normal.
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Epidemiologi
8 $elainan arah yang 'arang ter'ai i %nonesia.
8 Statistik i &merika menun'ukkan 0.6-1.6orang't !enuuk menerita olisitemia era.
8 /aki-laki ? !erem!uan
8 %nsiensi (erusia 50-70 tahun.
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Patofsiologi
8 enemuan mutasi JAK2V617Fmeru!akan hal yang !enting!aa etio!atogenesis!olisitemia @era+ an mem(uat
iagnosis !olisitemia @era le(ihmuah.
8 aa !olisitemia @era ter'aimutasi yang terletak !aa
!osisi 617 617A; sehingga!aa !asien !olisitemia @eraserum eritro!oetinnya renah
yaitu B m#m/+ serumeritro!oitin normal aalah -
26 m#m/.
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Dierential Diagnosis
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Penatalaksanaan
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