Patologia del-higado
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Patología del HígadoPatología del Hígado
Dr. Juan Luis Rojas PavezDr. Juan Luis Rojas Pavez
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Hígado Hígado
Se encuentra entre el aparato digestivo y el Se encuentra entre el aparato digestivo y el resto del cuerporesto del cuerpo
Peso: 1.400 – 1.600 gr. (2,5 % del peso Peso: 1.400 – 1.600 gr. (2,5 % del peso corporal)corporal)
Aporte sanguíneo: 60-70% vena portaAporte sanguíneo: 60-70% vena porta
30-40% arteria hepática30-40% arteria hepática
25% del gasto cardiaco25% del gasto cardiaco
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Arquitectura MicroscópicaArquitectura MicroscópicaLobulillos hepáticosLobulillos hepáticos
Acinos hepáticosAcinos hepáticos
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Funciones Funciones
Metabolismo de los carbohidratosMetabolismo de los carbohidratos
Metabolismo lipídicoMetabolismo lipídico
Metabolismo proteicoMetabolismo proteico
Síntesis de bilisSíntesis de bilis
DepósitoDepósito
DestoxificaciónDestoxificación
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Enfermedad HepáticaEnfermedad Hepática
Entidades clínicas principales:Entidades clínicas principales:
Hepatitis agudaHepatitis aguda
Hepatitis crónicaHepatitis crónica
ColestasisColestasis
Cirrosis Cirrosis
Insuficiencia Hepática (ictericia, coma, diátesis hemorrágica
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Causas de HepatopatíaCausas de Hepatopatía
Toxinas (alcohol y fármacos)Toxinas (alcohol y fármacos)
Infecciones (virus, bacterias, parásitos)Infecciones (virus, bacterias, parásitos)
Trastornos vasculares y de excreción biliarTrastornos vasculares y de excreción biliar
Tumores primarios y metástasisTumores primarios y metástasis
Enfermedad
Hepática
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Enfermedad hepática Enfermedad hepática según su origensegún su origen
PrimariaPrimariaHepatitis viralHepatitis viral
Carcinoma hepáticoCarcinoma hepático
SecundariaSecundariaInsuficiencia cardiacaInsuficiencia cardiaca
Cáncer diseminadoCáncer diseminado
AlcoholismoAlcoholismo
Infecciones extra-hepáticasInfecciones extra-hepáticas
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Patrones de respuesta del hígadoPatrones de respuesta del hígadofrente a las noxasfrente a las noxas
NecrosisNecrosisNecrosis FocalNecrosis Focal
Necrosis ZonalNecrosis Zonal
Necrosis Sub-masivaNecrosis Sub-masiva
Necrosis masivaNecrosis masiva
DegeneraciónDegeneración
InflamaciónInflamación
RegeneraciónRegeneración
Fibrosis Fibrosis
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Necrosis FocalNecrosis Focal
Centrolobulillar (tóxicas)Centrolobulillar (tóxicas)
Mesozonal (fiebre amarilla)Mesozonal (fiebre amarilla)
Periportal (fósforo, eclampsia)Periportal (fósforo, eclampsia)
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Hepatitis Hepatitis
AgudaAguda
CrónicaCrónica
Etiología:Etiología:VirusVirus
Trastornos autoinmunesTrastornos autoinmunes
Reacciones farmacológicasReacciones farmacológicas
Alcohol Alcohol
GranulomatosasGranulomatosas
Clínica e histología: Comunes, independiente Clínica e histología: Comunes, independiente de la etiología de la etiología
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Hepatitis viralHepatitis viral
Virus A y E (vía oro-fecal)Virus A y E (vía oro-fecal)
Virus B, C, D y G (vía parenteral)Virus B, C, D y G (vía parenteral)
Virus A
Virus B
Hepatitis Aguda
Hepatitis crónica
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Hepatitis aguda viralHepatitis aguda viral
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Hepatitis AgudaHepatitis Aguda
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Hepatitis Aguda Hepatitis Aguda Necrosis PuenteNecrosis Puente
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Hepatitis Colestásica Hepatitis Colestásica cuerpos de Councilmancuerpos de Councilman
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Hepatitis ColestásicaHepatitis Colestásica
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Hepatitis alcohólicaHepatitis alcohólicacélulas balonadas con cuerpos de Mallory células balonadas con cuerpos de Mallory
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Hepatitis alcohólicaHepatitis alcohólica
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Hepatitis B orceina (+)Hepatitis B orceina (+)
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Hepatitis aguda Hepatitis aguda necrosis focal lobulillarnecrosis focal lobulillar
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Hepatitis viral crónicaHepatitis viral crónica
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Hepatitis Crónica ActivaHepatitis Crónica Activatinción Massontinción Masson
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Hepatitis Crónica ActivaHepatitis Crónica Activatinción Massontinción Masson
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Hepatitis crónica activaHepatitis crónica activa
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Hepatitis Crónica PersistenteHepatitis Crónica Persistente
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Hepatitis crónica activaHepatitis crónica activa
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Hepatitis tuberculosa (Miliar)Hepatitis tuberculosa (Miliar)
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Hepatitis granulomatosaHepatitis granulomatosa
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Cirrosis Cirrosis
Es la condición caracterizada por fibrosis, Es la condición caracterizada por fibrosis, nódulos de regeneración y alteración de la nódulos de regeneración y alteración de la arquitectura vascular con shunts porto-arquitectura vascular con shunts porto-cava.cava.
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Cirrosis - ClasificaciónCirrosis - Clasificación1.1. Según factor etiológico:Según factor etiológico:
Cirrosis alcohólicaCirrosis alcohólicaCirrosis post-hepatitisCirrosis post-hepatitisCirrosis criptogenéticaCirrosis criptogenéticaCirrosis biliar primariaCirrosis biliar primariaCirrosis biliar secundariaCirrosis biliar secundariaCirrosis pigmentariaCirrosis pigmentariaCirrosis cardiacaCirrosis cardiacaCirrosis sifilíticaCirrosis sifilíticaCirrosis enfermedad de WilsonCirrosis enfermedad de Wilson
2.2. Según morfología:Según morfología:MicronodularMicronodularMacronodularMacronodular
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Causas de cirrosisCausas de cirrosis
Enfermedad hepática alcohólicaEnfermedad hepática alcohólica 60-70%60-70%
Hepatitis viralHepatitis viral 10% 10%
Enfermedades biliaresEnfermedades biliares 5-10% 5-10%
Hemocromatosis primariaHemocromatosis primaria 5% 5%
Enfermedad de WilsonEnfermedad de Wilson rara rara
Deficiencia de alfa1 antitripsina(AAT)Deficiencia de alfa1 antitripsina(AAT) rara rara
Cirrosis criptogenéticaCirrosis criptogenética 10-15%10-15%
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Cirrosis macronodularCirrosis macronodular
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Cirrosis micronodularCirrosis micronodular
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Hipertensión portalHipertensión portal
Es el aumento de la resistencia al flujo de Es el aumento de la resistencia al flujo de la sangre portal. la sangre portal.
Causas:Causas:– Pre-hepáticasPre-hepáticas– Intra-hepáticasIntra-hepáticas– Post-hepáticasPost-hepáticas
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Ictericia Ictericia
Definición: Definición: Es un signo clínico caracterizado por coloración Es un signo clínico caracterizado por coloración amarilla y/o amarillo-verdoso de piel, mucosas y amarilla y/o amarillo-verdoso de piel, mucosas y escleras.escleras.
Clasificación:Clasificación:Pre-hepáticaPre-hepática
Intra-hepáticaIntra-hepática
Post-hepáticaPost-hepática
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Enfermedades de depósitosEnfermedades de depósitos
HemocromatosisHemocromatosisPrimaria (hereditaria)Primaria (hereditaria)
Secundaria (alcoholismo, transfusiones)Secundaria (alcoholismo, transfusiones)
Enfermedad de WilsonEnfermedad de Wilson
Deficiencia de alfa1 antitripsina (cirrosis Deficiencia de alfa1 antitripsina (cirrosis hepática, enfisema panacinar)hepática, enfisema panacinar)
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Hemocromatosis Hemocromatosis
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hemocromatosishemocromatosis
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amiloidosisamiloidosis
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Tumores hepáticosTumores hepáticosBenignosBenignos
Adenomas hepáticos (anticonceptivos)Adenomas hepáticos (anticonceptivos)
Adenomas de las vías biliaresAdenomas de las vías biliares
Hemangiomas hepáticosHemangiomas hepáticos
MalignosMalignosPrimariosPrimarios
Carcinoma Hepatocelular (cirrosis, hepatitis B y micotoxinas–Carcinoma Hepatocelular (cirrosis, hepatitis B y micotoxinas–aspergillus flabus-aflotoxina)aspergillus flabus-aflotoxina)
Colangiocarcinoma Colangiocarcinoma
HepatoblastomaHepatoblastoma
Hemangiosarcoma Hemangiosarcoma
SecundariosSecundariosMetástasis de: (pulmón,mama, tracto digestivo,linfomas y Metástasis de: (pulmón,mama, tracto digestivo,linfomas y leucemias) leucemias)
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Pseudotumores Pseudotumores
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Hidatidosis Hidatidosis
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Absceso hepático por colangitisAbsceso hepático por colangitis
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Abseso hepático (pileflebitis)Abseso hepático (pileflebitis)
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Tumores benignos del hígadoTumores benignos del hígado
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Hemangioma Hemangioma
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Tumores malignos PrimariosTumores malignos Primarios
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Carcinoma HepatocelularCarcinoma Hepatocelular
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Carcinoma HepatocelularCarcinoma Hepatocelular
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Carcinoma Hepatocelular difusoCarcinoma Hepatocelular difuso
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Carcinoma Hepatocelular difusoCarcinoma Hepatocelular difuso
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Carcinoma Hepatocelular masivoCarcinoma Hepatocelular masivo
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Colangiocarcinoma Colangiocarcinoma
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Hepatoblastoma Hepatoblastoma
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Tumores malignos secundariosTumores malignos secundarios
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