SEQUELAS COGNITIVAS APÓS TRATAMENTO DOS TUMORES DO SISTEMA NERVOSO CENTRAL DA INFÂNCIA
Tumores do Sistema Nervoso Central aula ufpa
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Transcript of Tumores do Sistema Nervoso Central aula ufpa
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Tumores do Sistema Nervoso Central
Prof. Msc. José Maria Abreu Jr
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TUMORES DO SNC
• INCIDÊNCIA ANUAL: INTRACRANIANOS – 10 a 17/ 100.000
pessoasINTRAESPINAIS – 1 a 2/ 100.000 pessoas
• ½ a ¾ TUMORES PRIMÁRIOS
restante é METASTÁTICO
• TUMORES SNC – 20% dos CÂNCERES em criança
• 70% TUMORES SNC INFRATENTORIAIS- crianças• 70% TUMORES SNC SUPRATENTORIAIS- adultos
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TUMORES DO SISTEMA NERVOSO CENTRAL
CARACTERÍSTICAS ÚNICAS1. Diferente DISTINÇÃO entre BENIGNO/MALIGNO
GLIOMAS com histopatologia benigna ( atipias discretas, crescimento lento)
CURSO CLÍNICO E PROGNÓSTICO pobres
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2. RESSECÇÃO CIRÚRGICA COMPLETA nos GLIOMAS INFILTRANTES sem déficit neurológico – limitada
3. TOPOGRAFIA LESIONAL pode ser letal, independente do Tipo Histológico
4. DISSEMINAÇÃO diferente:METÁSTASES extra-SNC raras
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TUMORES DO SISTEMA NERVOSO CENTRAL
GRAUS DE MALIGNIDADE
Malignidade biológica ( ou histológica )
Malignidade clínica
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TUMORES DO SISTEMA NERVOSO CENTRAL
MALIGNIDADE HISTOLÓGICA
Diferenciação Celular
Parênquima tumoral ( células neoplásicas )
Estroma ( tecido de sustentação e vasos sangüíneos )
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TUMORES DO SISTEMA NERVOSO CENTRAL
Todos os tumores possuem dois componentes básicos:
1) as células neoplásicas que compreendem o parênquima do tumor;
2) o estroma, formado por tecido de sustentação e vasos sanguíneos.
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TUMORES DO SISTEMA NERVOSO CENTRAL
O elemento parenquimatoso é o mais importante por ser o componente em proliferação. O estroma fornece o suporte estrutural para o parênquima e abriga os vasos sanguíneos que nutrem as células tumorais sendo de particular importância nos estágios de desenvolvimento do tumor.
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TUMORES DO SISTEMA NERVOSO CENTRAL
Tumores de baixo grau (benignos) : bem diferenciados.
Tumores alto grau (malignos) : células indiferenciadas.
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TUMORES DO SISTEMA NERVOSO CENTRAL
Padrões de CrescimentoTumores Expansivos
O crescimento por expansão ocorre ao redor de um núcleo central, tende a assumir um formato esférico e comprime e/ou destrói tecidos adjacentes.
Estes tumores apresentam limites bem definidos com separação nítida entre os tecidos normal e neoplásico. Exemplos: schwannomas, meningeomas e ependimomas.
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TUMORES DO SISTEMA NERVOSO CENTRAL
Padrões de CrescimentoTumores Infiltrativos
O crescimento por infiltração se dá para o interior do interstício do tecido circundante e a extensão dessa infiltração vai depender basicamente do tipo de tumor e da arquitetura dos tecidos adjacentes. Podem ser circunscritos ou difusos.
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TUMORES DO SISTEMA NERVOSO CENTRAL
Padrões de PropagaçãoPropagação por continuidade
Propagação sem perder contato com a massa original. Podem ocorrer ao longo da superfície ou ao longo de tratos de fibras nervosas.
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TUMORES DO SISTEMA NERVOSO CENTRAL
Propagação por metástase
Qualquer crescimento tumoral à distância resultante da transferência por via sanguínea, linfática ou liquórica, bem como pela implantação cirúrgica de células tumorais destacadas do foco primário.
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TUMORES DO SISTEMA NERVOSO CENTRAL
MALIGNIDADE CLÍNICA É determinada pela malignidade
histológica associada aos seguintes fatores:
aumento do volume tumoral. reações do tecido cerebral
circundante (edema cerebral).
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TUMORES DO SISTEMA NERVOSO CENTRALMALIGNIDADE CLÍNICA
efeito de massa conseqüente à hipertensão intracraniana local ou generalizada ( hérnia cerebral ).
ação sobre o tráfego liquórico ( hidrocefalia obstrutiva ). ação sobre os vasos sangüíneos
(infartos). ação sobre centros neurológicos
vitais.
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TUMORES PRIMÁRIOS DO SNC• GLIOMAS: ASTROCITOMAS
OLIGODENDROGLIOMAS EPENDIMOMAS
TUMORES PLEXO CORIÓIDE TUMORES EMBRIONÁRIOS TUMORES DA PINEAL
• TUMORES GERMINATIVOS• MENINGEOMAS• TUMORES DOS NERVOS CRANIANOS E
ESPINAIS
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Astrocitoma Difuso
OMS grau II
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Fibrilar
• Atípia nuclear é critério diagnóstico.
• Atividade mitótica, necrose e formação de vasos – AUSENTES.
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Gemistocítico
• Mais que 20% de Gemistócitos
• Tendem a caminhar para o anaplásico, portanto tem potencial maior para evoluir para grau III.
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Astrocitoma Anaplásico
OMS Grau III
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Glioblastoma
OMS grau IV
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Astrocitoma Pilocítico
Grau I da OMS
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Oligodendroglioma
OMS grau II
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Oligodendroglioma Anaplásico
OMS grau III
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Oligoastrocitoma
OMS grau II
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Ependimoma
OMS Grau II
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Ependimoma Anaplásico
OMS Grau III
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Ependimoma Mixopapilar
OMS Grau I
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MENINGIOMAS
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Não cai na prova de residência, mas é bom saber...
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