Sociedad Hondureña de Epilepsia Capítulo de la ILAE
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Transcript of Sociedad Hondureña de Epilepsia Capítulo de la ILAE
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Sociedad Hondureña de Epilepsia
Capítulo de la ILAE
Dra. Claudia AmadorDr Marco Tulio Medina
Dra. Sofia Dubon
The Flag of Honduras
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Honduran Epilepsy Society
1. Dr. Claudia Amador * President
2. Dr. Heike Hesse Vice President
3. Prof. Marco T. Medina Past President
4. Dr. Reyna Duron Secretariat
5. Dr. Lazaro Molina Treasurer
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HONDURAS
Is a Central America Country with a Population of 8 millions
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Health Care Three Health Systems in
Honduras:1. Ministry of Health 2. Social Security for
state workers and others
3. Private Hospitals
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Neurological Care
• There was one neurologist per 325,000 inhabitants in 1998
• Neurological diseases account for approx. 20% of the medical consultations in hospitals
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Formación de Neurólogos y Epileptólogos WFN
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Epidemiología (Medina et al Epilepsia 2003, 2005)
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TREATMENT
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Status Epilepticus
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Proyecto Demostrativo en Honduras: Brecha de Tratamiento
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Community Intervention (Medina et al 2010, submitted)
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Significant reduction of Epilepsy due to NCC (36% versus 13.9%)
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Neuroepidemiology Studies
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The Salama Epilepsy StudyETIOLOGY OF EPILEPSY (n=90)
Neurocysticercosis 37%
Cryptogenic (occult) 30%
Idiopathic 8%
Perinatal brain damage 8 %Head trauma 3%CNS malformations 2%Vascular 2%
Other neuroinfections 2%Other causes* 8%
Other causes: inespecific calcified lesions, alcohol toxicity, inespectific intraventricular cyst, multifactorial.
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Government involvement
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Epilepsy Surgery Program in Honduras
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Disease JME CAE
Phenotype
Myoclonic, grand mal epilepsy, 1/3 with absences
Pyknoleptic (2-200/day) absences of
childhood
Pathology Microdysgenesis-Displaced and dystopic cells
Normal
Gene Myoclonin/EFHC1
GABRB3
Transgenic mice
KO mice replicate pathology and susceptibility
KO mice replicate epilepsy
Epilepsy GenesEpilepsy genes found in Honduras
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Suzuki et al.Nature Genetics, 2004
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Tanaka M, Olsen RW, Medina MT, et al Am J Hum Genet. 2008 Jun;82(6):1249-61.
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Medina MT et al. Neurology 2008
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Group of Patients
• Epilepsy (FUNDACION HONDURENA DE EPILEPSIA)
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Publicaciones (Books and Journals
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Latin American Epilepsy Academy (Academia Latino Americana de Epilepsia ALADE) Founded in Sao Paulo Feb. 27th, 2007