endokrinuli sistemis, kvebisa da nivTierebaTa cvlis ... · ginekomastia (N 62) E hipoparaTireozi ar...
Transcript of endokrinuli sistemis, kvebisa da nivTierebaTa cvlis ... · ginekomastia (N 62) E hipoparaTireozi ar...
184
avadmyofobaTa saerTaSoriso klasifikacia
Tavi IV.
endokrinuli sistemis, kvebisa da nivTierebaTa cvlis
darRveviT gamowveuli avadmyofobani
(E00-E90)
SeniSvna: simsivneebi (funqciurad aqtiuri Tu ara aqtiuri) Setanilia II klasSi. am klasSi SemavaliSesabamisi kodebi (magaliTad, E05.8, E07.0, E16-E31,E34.) aucileblobis(saWiroebis) SemTxvevaSi SeiZleba gamoyenebuli iyos, rogorc damatebiTi(kodebi) funqciurad aqtiuri simsivneebisa da eqtopiuri endokrinuliqsovilebis da, agreTve, sxva rubrikebSi Setanil simsivneebTan da sxvapaTologiebTan dakavSirebuli endokrinuli jirkvlis hi per- dahipofunqciis aRsaniSnavad.
ar igulisxmeba: orsulobis, mSobiarobis da loginobis xanis garTulebani (O00-O09)klinikuri da laboratoriuli gamokvlevebiT gamovlenili
simptomebi, niSnebi da normidan gadaxrebi, romlebic ar aris Setanili sxvarubrikebSi (R00-R99)
nayofisa da axalSobilis endokrinuli funqciebisa da nivTierebaTa cvlisgardamavali specifikuri darRvevebi (P70-P74)
es klasi Seicavs Semdeg blokebs:
E00-E07 farisebri jirkvlis avadmyofobaniE10-E14 Saqriani diabetiE15-E16 glukozis regulaciisa da pankreasis Sinagani sekreciis funqciis sxva darRvevebiE20-E35 sxva endokrinuli jirkvlebis avadmyofobebiE40-E46 malnutricia (sakvebis arasakmao raodenobiT miReba)E50-E64 kvebiTi deficitis sxva saxeebiE65-E68 simsuqne da sxva saxis hiperalimentaciebi da Warbi kvebis sxva saxeebiE70-E90 nivTierebaTa cvlis darRvevebi
am Tavis varskvlaviani kategoriebi mocemulia Semdegi saxiT:
E35* endokrinuli jirkvlebis dazianebani im avadmyofobaTa dros, romlebic Setaniliasxva klasifikaciebSi
E90* kvebisa da nivTierebaTa cvlis darRvevebi im avadmyofobaTa dros,romelicüSetanilia sxva klasifikaciebSi
farisebri jirkvlis avadmyofobebi
(E00-E07)E
Tandayolili iod-deficituri sindromi
igulisxmeba: endemiuri mdgomareobani, rogorc uSualod dakavSirebuli bunebrivgaremoSi arsebul iodis deficitTan da, rogorc dedis organizmSi iodisdeficitis Sedegi. zogierTi aseTi mdgomareoba ar ganekuTvneba WeSmarithi poTireozs, aramed warmoadgens ganviTarebadi nayofis organizmSifarisebri jirkvlis hormonebis araadeqvaturi sekreciis Sedegs; SeiZleba
arsebobdes kavSiri Ciyvis gamomwvev bunebriv faqtorebTan.Tanmxlebi gonebrivi SezRudulobis identifikaciis aucileblobis SemTxvevaSigamoiyeneba damatebiTi kodi (F 70-F 79)ar igulisxmeba:iodis deficitiT gamowveuli subklinikuri hipoTireozi (E 02)
E
E00
185
endokrinuli sistemis, kvebisa da nivTierebaTa cvlis darRveviT gamowveuli avadmyofobani
E00.0 Tandayolili iod-deficituri sindromi, nevrologiuri formaendemiuri kretinizmi, nevrologiuri forma
E00.1 Tandayolili iod-deficituri sindromi, miqsedemuri formaendemuri kretinizmi:
. hipoTiroiduli
. miqsedemuri forma
E00.2 Tandayolili iod-deficituri sindromi, Sereuli tipiendemuri kretinizmi, Sereuli tipi
E00.9 Tandayolili iod-deficituri sindromi, dauzustebeliTandayolili iod-deficituri hipoTireozi, romelic sxvagvarad ar aris dazustebuli
endemurri kretinizmi, romelic sxvagvarad ar aris dazustebuli
Efarisebri jirkvlis iodis deficitTan dakavSirebuli dazianebani da
msgavsi mdgomareobani
ar igulisxmeba: Tandayolili iod-deficituri sindromi (E 00.-)subklinikuri iod-deficituri hipoTireozi (E 02)
E01.0 iodis deficitTan dakavSirebuli difuzuri (endemuri) CiyviE01.1 iodis deficitTan dakavSirebuli mravalkvanZovani (endemuri) Ciyvi
iodis deficitTan dakavSirebuli kvanZovani Ciyvi
E01.2 iodis deficitTan dakavSirebuli (endemuri) Ciyvi, dauzustebeliendemuri Ciyvi, romelic sxvagvarad ar aris dazustebuli
E01.8 iodis deficitTan dakavSirebuli farisebri jirkvlis sxva dazianebanida mdgomareobaniSeZenili iod-deficituri hipoTireozi, romelic sxvagvarad ar aris dazustebuli
E subklinikuri iod-deficituri hipoTireozi
E
hipoTireozis sxva formebi
ar igulisxmeba: iodis deficitTan dakavSirebuli hipoTireozi (E00-E02)samedicino procedurebis Semdeg ganviTarebuli hipoTireozi (E 89.0)
E03.0 Tandayolili hipoTireozi difuzuri CiyviTCiyvi (aratoqsiuri) Tandayolili:
. romelic, sxvagvarad ar aris dazustebuli
. parenqimuli
ar igulisxmeba: gardamavali Tandayolili Ciyvi normaluri funqciiT (P 72.0)E03.1 Tandayolili hipoTireozi Ciyvis gareSe
farisebri jirkvlis aplazia (miqsedemiT)
Tandayolili:. farisebri jirkvlis atrofia
. hipoTireozi, romelic sxvagvarad ar aris dazustebuli
E03.2 medikamentebiT da sxva egzogenuri nivTierebebiT gapirobebulihipoTireozi
mizezis identifikaciis aucileblobis SemTxvevaSi gamoiyeneba garegani mizezebis
damatebiTi kodi (klasi XX)
E03.3 postinfeqciuri hipoTireoziE03.4 farisebri jirkvlis atrofia (SeZenili)
ar igulisxmeba: farisebri jirkvlis Tandayolili atrofia (E 03.1)E03.5 miqsedemuri koma
E01
E02
E03
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avadmyofobaTa saerTaSoriso klasifikacia
E03.8 sxva saxis dazustebuli hipoTireoziE03.9 hipoTireozi, dauzustebeli
miqsedema, romelic sxvagvarad ar aris dazustebuli
aratoqsiuri Ciyvis sxva formebi
ar igulisxmeba:Tandayolili Ciyvi:
. romelic sxvagvarad araris dazustebuli
. difuzuri (E 03.0)
. parenqimuli
iodis-deficitTan dakavSirebuli Ciyvi (E 00-E 02)E04.0 aratoqsiuri difuzuri Ciyvi
Ciyvi, aratoqsiuri:
. difuzuri, (koloiduri)
. martivi
E04.1 aratoqsiuri erTkvanZiani Ciyvikoloiduri kvanZi (cisturi)(Tireoiduli)
aratoqsiuri erTkvanZovani Ciyvi
Tireoiduli (cisturi) kvanZi, romelic sxvagvarad ar aris dazustebuli
E04.2 aratoqsiuri mravalkvanZovani Ciyvicisturi Ciyvi, romelic sxvagvarad ar aris dazustebuli
mravalkvanZovani (cisturi) Ciyvi, romelic sxvagvarad ar aris dazustebuli
E04.8 aratoqsiuri Ciyvis sxva dazustebuli formebiE04.9 aratoqsiuri Ciyvi, dauzustebeli formebi
Ciyvi, romelic sxvagvarad ar aris dazustebuli
kvanZovani Ciyvi (aratoqsiuri), romelic sxvagvarad ar aris dazustebuli
ETireotoqsikozi [hiperTireozi]
ar igulisxmeba: qronikuli Tiroiditi gardamavali TireotoqsikoziT (E 06.2)neonataluri Tireotoqsikozi (P 72.1)
E05.0 Tireotoqsikozi difuzur CiyviTegzoftalmuri an toqsiuri Ciyvi, romelic sxvagvarad ar aris dazustebuli
greivsis avadmyofoba
difuzuri toqsiuri Ciyvi
E05.1 Tireotoqsikozi farisebri jirkvliseuli toqsiuri kvanZiTTareotoqsikozi erTkvanZovani toqsiuri CiyviT
E05.2 Tireotoqsikozi mravalkvanZovani toqsiuri Ciyvitoqsinuri kvanZovani Ciyvi, romelic sxvagvarad ar aris dazustebuli
E05.3 Tireotoqsikozi, eqtopiuri Tireoiduli qsovilidanE05.4 Tireotoqsikozi xelovnuriE05.5 Tiroiduli krizi anu SetevaE05.8 Tireotoqsikozis sxva formebi
Tireo-mastimulebeli hormonis Warbi produqcia
Tu mizezis identifikaciis survili gagvT, gamoiyeneT damatebiTi garegani mizezebis kodi (Tavi XX)
E05.9 Tireotoqsikozi dauzustebelihiperTireozi, romelic sxvagvarad ar aris dazustebuli
gulis Tireotoqsinuri avadmyofoba + (I43.8*)
Tiroiditi
ar igulisxmeba: mSobiarobis Semdgomi Tiroiditi (O 90.5)
E04
E05
E06
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endokrinuli sistemis, kvebisa da nivTierebaTa cvlis darRveviT gamowveuli avadmyofobani
E06.0 mwvave Tiroiditifarisebri jirkvlis abscesi
Tiroiditi:. Cirqovani (piogenuri). supuraciuliinfeqciuri agentis identifikaciis aucileblobis SemTxvevaSi gamoiyeneba damatebiTi
kodi (B 95-B 97)E06.1 qvemwvave Tiroiditi
Tireoiditi:
. de kervenis
. giganturujredovani
. granulomatozuri
. araCirqovani
ar igulisxmeba: autoimunuri Tiroiditi (E 06.3)E06.2 qronikuli Tiroiditi gardamavali TireotoqsikoziT
ar igulisxmeba: autoimunuri Tireoiditi (E 06.3)E06.3 autoimunuri Tiroiditi
haSimotos Tiroiditi
haSitoqsikozi (gardamavali)limfadenoiduri Ciyvilimfocituri Tireoiditi
limfomatozuri Ciyvi
E06.4 wamliT gamowveuli TireoiditiTu wamlis identifikaciis aucileblobis SemTxvevaSi damatebiTi garegani mizezebis kodi
(klasi XX)
E06.5 sxva saxis qronikuli TiroiditebiTiroiditi:. qronikuli. romelic sxvagvarad ar aris dazustebuli. fibrozuli. mkvrivi
. ridelis
E06.9 Tiroiditi dauzustebeliE
farisebri jirkvlis sxva avadmyofobani
EE07.0 kalcitoninis hipersekrecia
farisebri jirkvlis C-ujredebis hiperplazia
Tireokalcitoninis hipersekrecia
E07.1 dishormonuli Ciyviojaxuri dishormogenuli Ciyvi
pendredis sindromiar igulisxmeba: Tandayolili gardamavali Ciyvi farisebri jirkvlis normaluri funqciiT
(P 72.0)E07.8 farisebri jirkvlis sxva dauzustebeli avadmyofobani
farisebri jirkvlis hormonebis SemkavSirebuli globulinis paTologia
sisxlis Caqceva farisebr jirkvalSifarisebri jirkvlis infarqti
avadmyofuri euTiroiduli sindromi
E07.9 farisebri jirkvlis daavadebebi, dauzustebeli
E07
188
avadmyofobaTa saerTaSoriso klasifikacia
Saqriani diabeti
(E10-E14)
samkurnalo preparatis identifikaciis aucileblobis SemTxvevaSi gamoiyeneba damatebiTi gareganimizebis kodi (klasi XX)
qvemoT aRniSnuli meoTxe niSnebi gamoiyeneba E10 - E14 rubrikebTa erTad:
. 0 komiT
diabeturi. koma ketoacidoziT an mis gareSe. hiperosmosuri koma. hipoglikemiuri komahiperglikemiuri koma, romelic sxvagvarad ar aris dazustebuli
. 1 ketoacidoziT
diabeturi:. acidozi. ketoacidozi
. 2† Tirkmlebis dazianebiT
diabeturi nefropaTia (N 08.3*)intrakapilaruli glomerulonefrozi (N 08.3*)kimelstil-uilsonis sindromi (N 08.3*)
. 3† Tvalebis dazianebiT
diabeturi:. kataraqta (H 28.0*). retinopaTia (H 36.0*)
. 4† nevrologiuri garTulebebiT
diabeturi:. amiotrofia (G 73.0*). avtonomiuri neiropaTia (G 99.0*). mononeiropaTia (G 59.0*). polineiropaTia (G 63.2*). avtonomiuri (G 99.0*)
. 5 periferiuli cirkulaciis moSliT
diabeturi:. gangrena. periferiuli angiopaTia + (I79.2*). wyluli
. 6 sxva saxis specifikuri garTulebebiT
diabeturi arTropaTia + (M 14.2*). neiropaTiuri + (M 14.6*)
. 7 mravlobiTi garTulebebiT
. 8 dauzustebeli garTulebebiT
. 9 garTulebebis gareSe
insulindamokidebuli Saqriani diabeti
[ix. gv. 188 qvedanayofebisaTvis]
igulisxmeba: diabeti (Saqriani):. labiluri. iuvenilur asakSi. ketozisadmi midrekilebiT. tipi I
ar igulisxmeba: Saqriani diabeti:. arasakmaris kvebasTan dakavSirebuli (E 12.-). neonataluri (P 70.2). orsulobis, mSobiarobis dros da mSobiarobis Semdgom periodSi (O24.-)glukozuria:
E10
189
endokrinuli sistemis, kvebisa da nivTierebaTa cvlis darRveviT gamowveuli avadmyofobani
. romelic sxvagvarad ar aris dazustebuli (R 81)
. Tirkmlismieri (E 74.8)daqveiTebuli tolerantoba glukozis mimarT (R 73.0)postoperaciuli hipoinsulinemia (E 89.1)
Einsulindamoukidebeli Saqriani diabeti
[ix. gv. 188 qvedanayofebisaTvis]
igulisxmeba: diabeti (Saqriani)(simsuqnis gareSe)(simsuqniT):. dawyebuli mozrdilTa asakSi. dawyebuli mowifulobis periodSi. ketozisadmi midrekilebis gareSe. stabiluri. tipi IIaxalgazrdaTa insulindamoukidebuli diabeti
ar igulisxmeba: Saqriani diabeti:. arasakmaris kvebasTan dakavSirebuli (E 12.-). neonataluri (P 70.2). orsulobis, mSobiarobis dros da mSobiarobis Semdgom periodSi (O24.-)glukozuria:. romelic sxvagvarad ar aris dazustebuli (R 81). Tirkmlismieri (E 74.8)daqveiTebuli tolerantoba glukozis mimarT (R 73.0)postoperaciuli hipoinsulinemia (E 89.1)
arasakmaris kvebasTan dakavSirebuli Saqriani diabeti
[ix. gv. 188 qvedanayofebisaTvis]
igulisxmeba: arasakmaris kvebasTan dakavSirebuli Saqriani diabeti:. insulindamokidebuli
. insulindamoukidebeli
ar igulisxmeba:Saqriani diabeti orsulobis, mSobiarobis dros da mSobiarobis SemdgomperiodSi (O 24.-)
glukozuria:. romelic sxvagvarad ar aris dazustebuli (R 81). Tirkmlismieri (E 74.8)daqveiTebuli tolerantoba glukozis mimarT (R 73.0)neonataluri Saqriani diabeti (P 70.2)
postoperaciuli hipoinsulinemia (E 89.1)
ESaqriani diabetis sxa dazustebuli formebi
[ix. gv. 188 qvedanayofebisaTvis]ar igulisxmeba: Saqriani diabeti:
. insulindamokidebuli (E 10.-)
. arasakmaris kvebasTan dakavSirebuli (E 12.-)
. neonataluri (P 70.2)
. insulindamoukidebeli (E 11.-)
. orsulobis, mSobiarobis dros da mSobiarobis Semdgom periodSi (O24.-)glukozuria:. romelic sxvagvarad ar aris dazustebuli (R 81). Tirkmlismieri (E 74.8)daqveiTebuli tolerantoba glukozis mimarT (R 73.0)postoperaciuli hipoinsulinemia (E 89.1)
dauzustebeli Saqriani diabeti
E11
E12
E13
E14
190
avadmyofobaTa saerTaSoriso klasifikacia
[ix. gv. 188 qvedanayofebisaTvis]
igulisxmeba: diabeti, romelic sxvagvarad ar aris dazustebuliar igulisxmeba: Saqriani diabeti:
. insulindamokidebuli (E 10.-)
. arasakmaris kvebasTan dakavSirebuli (E 12.-)
. neonataluri (P 70.2)
. insulindamoukidebeli (E 11.-)
. orsulobis, mSobiarobis da mSobiarobis Semdgom periodSi (O 24.-)glukozuria:. romelic sxvagvarad ar aris dazustebuli (R 81). Tirkmlismieri (E 74.8)daqveiTebuli tolerantoba glukozis mimarT (R 73.0)postoperaciuli hipoinsulinemia (E 89.1)
glukozis regulaciisa da pankreasis Sinagani sekreciis funqciis
sxva darRvevebi
(E15-E16)E
aradiabeturi hipoglikemiuri koma
wamlismieri insulinuri koma aradiabetian avadmyofebSi
hiperinsulinizmi hipoglikemiuri komiThipoglikemiuri koma, romelic sxvagvarad ar aris dazustebuliTu wamliT gamowveulia da gsurT wamlis identifikacia, gamoiyeneT damatebiTi garemizezebis kodi (Tavi XX)
Epankreasis Sinagani sekreciis sxva darRvevebi
EE16.0 wamlismieri hipoglikemia komis gareSe
samkurnalo saSualebis identifikaciis aucileblobis SemTxvevaSi gamoiyeneba damatebiT
gare mizezebis kodi (Tavi XX)
E16.1 hipoglikemiebis sxva formebifunqciuri ara hiperinsulinemiuri hipoglikemia
hiperinsulinizmi. romelic sxvagvarad ar aris dazustebuli. funqciuripankreasis kunZulebis beta-ujredebis hiperplazia, romelic sxvagvarad ar aris dazustebuli
encelofaTia hipoglikemiuri komis Semdeg
E16.2 hipoglikemia, dauzustebeliE16.3 glukagonis gaZlierebuli sekrecia
pankreasis endokrinuli ujredebis hiperplazia glukagonis gaZlierebuli sekreciiT
E16.8 pankreasis Sinagani sekreciis sxva dazustebuli darRvevebihipergastrinemia
endokrinuli pankreasis mier gaZlierebuli sekrecia:. zrdis hormonis "rilizing hormonis". pankreasuli polipeptidis. somatostatinis. vazoaqtiuri nawlavuri polipeptidis
zolinger-elisonis sindromi
E16.9 pankreasis Sinagani sekreciis darRveva dauzustebelikunZulakebis ujredebis hiperplazia, romelic sxvagvarad ar aris dazustebuli
pankreasis endokrinuli ujredebis hiperplazia, romelic sxvagvarad ar aris dazustebuli
E15
E16
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endokrinuli sistemis, kvebisa da nivTierebaTa cvlis darRveviT gamowveuli avadmyofobani
sxva endokrinuli jirkvlebis avadmyofobebi
(E20-E35)ar igulisxmeba: galaktorea (N 64.3)
ginekomastia (N 62)
E hipoparaTireozi
ar igulisxmeba: di jorjis sindromi (D 82.1)samedicino proceduris Semdgomi hipoparaTireozi (E 89.2)tetania, romelic sxvagvarad ar aris dazustebuli (R 29.0)axalSobilTa gardamavali hipoparaTireozi (P 71.4)
E20.0 odiopaTiuri hipoparaTireoziE20.1 fsevdohipoparaTireoziE20.8 hipoparaTireozis sxva formebiE20.9 hipoparaTireozi, dauzustebeli
paraTireoiduli tetania
hiperparaTireozi da farisebraxlo jirkvlebis sxva darRvevebi
ar igulisxmeba: osteomalacia:
. mozrdilTa (M 83.-)
. bavSvTa da mozardTa (E 55.0)E21.0 pirveladi hiperparaTireozi
farisebraxlo jirkvlebis hiperplazia
generalizebuli fibrozuli cisturi ostiti [fon reklinhauzenis Zvlis avadmyofoba]
E21.1 meoradi hiperparaTireoidozi, romelic ar aris Setanili sxva klasifikaciebSiar igulisxmeba: Tirkmlismieri warmoSobis meoradi hiperparaTireozi (N 25.8)
E21.2 hiperparaTireozis sxva formebiar igulisxmeba:ojaxuri hipokalciuriuli hiperkalciemia (E 83.5)
E21.3 hiperparaTireozi, dauzustebeliE21.4 farisebraxlo jirkvlebis sxva dazustebuli avadmyofobebiE21.5 farisebraxlo jirkvlebis avadmyofoba, dauzustebeliE
hipofizis hiperfunqcia
ar igulisxmeba: kuSingis sindromi (E 24.-)nelsonis sindromi (E 24.1)Warbi produqcia:. adenokortikotropuli (akth)-is, romelic ar aris dakavSirebuli
kuSingis avadmyofobasTan (E 27.0). hipofizis akth-is (E 24.0). Tiroid-mastimulaciebuli hormonis (E 05.8)
E22.0 akromegalia da hipofizuri gigantizmiakromegaliasTan dakavSirebuli arTropaTia +(M 14.5*)zrdis hormonis Warbi produqciaar igulisxmeba: konstituciuri:
. gigantizmi (E 34.4)
. maRali tani (E 34.4)endokrinuli pankreasis mier zrdis hormonis "rilizingiz hormonis" gaZlierebuli sekrecia (E 16.8)
E22.1 hiperprolaqtinemiahiperprolaqtinemiis gamomwvevi samkurnalo saSualebis identifikaciis aucileblobis
SemTxvevaSi gamoiyeT gare mizezebis kodi (Tavi XX)
E20
E21
E22
192
avadmyofobaTa saerTaSoriso klasifikacia
E22.2 antidiurezuli hormonis araadeqvaturi sekreciis sindromiE22.8 hipofizis hiperfunqciebis sxva mdgomareobani
centraluri warmoSobis naadrevi sqesobrivi momwifeba
E22.9 hipofizis hiperfunqcia dauzustebeli
E hipofizis hipofunqcia da sxva darRvevebi
igulisxmeba: qvemoCamoTvlili mdgobareobani, miuxedavad imisa, dazianeba hipofizSiaTu hipoTalamusSi
ar igulisxmeba:procedurebis Semdeg aRmocenebuli hipopituitarizmi (E 89.3)E23.0 hipopituitarizmi
fertiluri evnuxoiduri sindromi
hipogonadotropuli hipogonadizmizrdis hormonis idiopaTiuri deficitiizolirebuli deficiti:. gonadotropinis
. zrdis hormonis
. hipofizis sxva hormonebis
kalmanis sindromilorein-levis dabali aRnagoba {qondriskacoba]hipofizis nekrozi (mSobiarobis Semdgomi)panhipopituitarizmihipofizuri:. kaxeqsia. ukmarisoba, romelic sxvagvarad ar aris dazustebuli. dabali tani (qondriskacoba). Sihenis sindromi
. simondsis avadmyofoba
E23.1 wamlismieri hipopituitarizmiwamlis identifikaciis aucileblobis SemTxvevaSi gamoiyeneba damatebiTi gare mizezebis
kodi (Tavi XX)
E23.2 uSaqro diabetiar igulisxmeba: nefrogenuli uSaqro diabeti (N 25.1)
E23.3 hipoTalamusis disfunqcia, romelic ar aris Setanili sxva klasifikaciebSiar igulisxmeba: prader-vilis sindromi (Q 87.1)
rasel-silveris sindromi (Q 87.1)E23.6 hipofizis sxva dazianebebi
hipofizis abscesi
adipozogenitaluri distrofia
E23.7 hipofizis dazianeba dauzustebeliE
kuSingis sindromi
EE24.0 hipofiz-damokidebuli kuSingis avadmyofoba
hipofizis akth-is Warbi produqcia
hipofiz-damokidebuli hiperadrenokorticizmi
E24.1 nelsonis sindromiE24.2 wamlismieri kuSingis sindromi
samkurnalo saSualebis identifikaciis SemTxvevaSi gamoiyeneba damatebiTi gare mizezebis
kodi (Tavi XX)
E24.3 eqtopiuri akth - sindromiE24.4 alkoholiT gamowveuli fsevdo-kuSingis sindromi
E23
E24
193
endokrinuli sistemis, kvebisa da nivTierebaTa cvlis darRveviT gamowveuli avadmyofobani
E24.8 sxva saxis kuSingis sindromiE24.9 kuSingis sindromi dauzustebeli
adrenogenitaluri darRvevebi
igulisxmeba:adrenogenitaluri sindromebi, virilizacia an feminizacia, SeZenili angapirobebuli Tirkmelzeda jirkvlis hiperplaziiT, romelicwarmoadgens hormonTa sinTezisaTvis aucilebeli fermentebis Tandayoliliukmarisobis Sedegs
qalis:. Tirkmelzeda jirkvlismieri fsevdohermafroditizmi. heteroseqsualuri naadrevi cru sqesobrivi momwifebamamakacis:
. izoseqsualuri naadrevi cru sqesobrivi momwifeba
. naadrevi makrogenitosomia prde cox (adreuli)
. naadrevi sqesobrivi momwifeba Tirkmelzeda jirkvlis hiperplaziiT
virilizacia (qalis)
E25.0 fermentebis deficitTan dakavSirebuli Tandayolili adrenogenitaliuridarRvevebiTirkmelzeda jirkvlebis Tandayolili hiperplazia21-hidroqsilazis deficiti
marilebis-kargviT mimdinare Tirkmelzeda jirkvlebis Tandayolili hiperplazia
E25.8 sxva adrenogenitaluri darRvevebiidiopaTiuri adrenogenitaliuri darRveva
Tu wamliT gamowveulia da wamlis identifikacia gsurT, gamoiyeneT damatebiTi gare
mizezebis kodi (Tavi XX)
E25.9 adrenogenitaliuri moSliloba, dauzustebeliadrenogenitaliuri sindromi, romelic sxvagvarad ar aris dazustebuli
Ehiperaldosteronizmi
EE26.0 pirveladi hiperaldosteronizmi
konis sindromi
pirveladi aldosteronizmi, gamowveuli Tirkmelzeda jirkvlebis ormxrivi hiperplaziiT
E26.1 meoradi hiperaldosteronizmiE26.8 sxva saxis hiperaldosteronizmi
barteris sindromi
E26.9 hiperaldosteronizmi, dauzustebeliE
Tirkmelzeda jirkvlis sxva darRvevebi
EE27.0 sxva adrenokortikuli zeaqtivoba
akth-is Warbi produqcia, romelic ar aris dakavSirebuli kuSingis avadmyofobasTan
ar igulisxmeba: kuSingis sindromi (E 24.-)E27.1 pirveladi adrenokortikuli ukmarisoba
adisonis avadmyofoba
autoimunuri adrenalitiar igulisxmeba: amiloidozi (E 85.-)
adisonis tuberkulozuri avadmyofoba (A 18.7)vaterpauz-frideriksenis sindromi (A 39.1)
E27.2 adisonuri krizi
E25
E26
E27
194
avadmyofobaTa saerTaSoriso klasifikacia
Tirkmelzeda jirkvlismieri krizi
adrenokortikuli krizi
E27.3 wamlismieri adrenokortikuli ukmarisobaTu wamlis identifikacia gsurT, isargebled damatebis gare mizezTa kodiT (Tavi XX)
E27.4 sxva da dauzustebeli adrnokortikuli ukmarisobaTirkmelzeda jirkvlis:
. sisxlCaqceva
. infarqtiadrenokortikuli ukmarisoba, romelic sxvagvarad ar aris dazustebulihipoaldosteronizmiar igulisxmeba: adrenoleikodistrofia (adison-Silteris)(E 71.3)
vaterhauz-fridriksenis sindromi (A 39.1)E27.5 Tirkmelzeda jirkvlis tvinovani Sris hiperfunqcia
Tirkmelzeda jirkvlis tvinovani Sris hiperplazia
kateqolaminebis hipersekrecia
E27.8 Tirkmelzeda sxva dazustebuli darRvevebikortizol-SemboWveli globulinis paTologia
E27.9 Tirkmelzeda jirkvlis funqciis darRveva, dauzustebeli
E sakvercxeebis disfunqcia
ar igulisxmeba: gonadotropinis izolaciuri deficiti (E 23.0) sakvercxis postproceduruli dazianeba (E 89.4)
E28.0 estrogenis siWarbeTu wamlismieria da wamlis identifikacia gsurT, isargebled damatebiTi gare mizezTa
kodiT (Tavi XX)
E28.1 androgenis siWarbesakvercxis androgenebis hipersekrecia
Tu wamlismieria da wamlis identifikacia gsurT, isargebled damatebiTi gare mizezTa
kodiT (Tavi XX)
E28.2 polikisturi sakvercxis sindromisklerokistuli sakvercxis sindromi
Stein-leventalis sindromi
E28.3 sakvercxis pirveladi ukmarisobaestrogenebis daqveiTebuli raodenoba
naadrevi menopauza, romelic sxvagvarad ar aris dazustebulirezistentuli sakvercxis sindromiar igulisxmeba: menopauzuri da qalTa klimaqsuri mdgomareobebi (N 95.1)
WeSmariti gonaduri disgenezia (Q 99.1)terneris sindromi (Q96.-)
E28.8 sakvercxis funqciis sxva darRvevebisakvercxis hiperfunqcia, romelic sxvagvarad ar aris dazustebuli
E28.9 sakvercxis funqciis moSliloba, dauzustebeli
E saTesle jirkvlis disfunqcia
ar igulisxmeba: androgenTa mimarT rezistentobis sindromi (E 34.5)azoospermia an oligospermia, romelic sxvagvarad ar aris dazustebuli (E 23.0)goanadotropinis izolirebuli deficiti (E 23.0)klainefelteris sindromi (Q 98.0-Q 98.2, Q 98.4)saTesleebis postproceduruli hipofunqcia (E 89.5)testikuluri feminizacia (sindromi)(E 34.5)
E28
E29
195
endokrinuli sistemis, kvebisa da nivTierebaTa cvlis darRveviT gamowveuli avadmyofobani
E29.0 saTesle jirkvlis hiperfunqciasaTeslis hormonebis hipersekrecia
E29.1 saTesle jirkvlis hipofunqciasaTeslis androgenebis defeqturi biosinTezi, romelic sxvagvarad ar
aris dazustebuli5-a -reduqtazis deficiti (mamakacur fsevdohermafroditizmTan erTad)testikuluri hipogonadizmi, romelic sxvagvarad ar aris dazustebuliTu wamlismieria da wamlis identifikacia gsurT, isargebled damatebiTi gare mizezTa
kodiT (Tavi XX)
E29.8 saTesle jirkvlis funqciis sxva moSlilobebiE29.9 saTeslis disfunqcia, dauzustebeli
sqesobrivi momwifebis darRvevebi, romelic ar aris Setanili sxva
klasifikaciebSi
EE30.0 sqesobrivi momwifebis Seferxeba
sqesobrivi simwifis konstituciuri Seferxeba
sqesobrivi ganviTarebis Seferxeba
E30.1 naadrevi sqesobrivi momwifebanaadrevi menstruaciaar igulisxmeba: olbrait (-makkunis)(-Sternbergis) sindromi (Q 78.1)
centraluri naadrevi sqesobrivi simwife (E 22.8)Tirkmelzeda jirkvlis Tandayolili hiperplazia (E 25.0)qalTa heteroseqsualuri naadrevi cru sqesobrivi simwife (E 25.-)mamakacTa izoseqsualuri naadrevi cru sqesobrivi simwife (E 25.-)
E30.8 sqesobrivi momwifebis sxva darRvevebisarZeve jirkvlis naadrevi momwifeba
E30.9 sqesobrivi momwifebis darRveva, dauzustebeli
poliglanduluri disfunqcia
ar igulisxmeba: ataqsia telangieqtazia (luis-baris) (G 11.3)miotonuri distrofia (Steniertis) (G 71.1)fsevdohipoparaTiroidizmi (E 20.1)
E31.0 autoimunuri poliglanduluri ukmarisobaSmidtis sindromi
E31.1 poliglanduluri hiperfunqciaar igulisxmeba:mravlobiTi endokrinuli adenomatozi (P 44.8)
E31.8 sxva saxis poliglanduluri disfunqciaE31.9 poliglanduluri disfunqcia, dauzustebeliE
Timusis avadmyofobebi
ar igulisxmeba: : : : : aplazia an hipoplazia imunodeficitTan erTad (D 82.1)miasTenia gravis (G 70.0)
E32.0 Timusis persistuli hiperplaziaTimusis hipertrofia
E32.1 Timusis abscesiE32.8 Timusis sxva avadmyofobebiE32.9 Timusis daavadeba, dauzustebeliE
E30
E31
E32
196
avadmyofobaTa saerTaSoriso klasifikacia
sxva endokrinuli darRvevebi
ar igulisxmeba: fsevdohipoparaTiroidizmi (E 20.1)E34.0 karcinoiduli sindromi
SeniSvna: Tu gsurT karcinoidul simsivnesTan dakavSirebuli funqciuri aqtivobis
identifikacia, SegiZliaT gamoiyenoT damatebiTi kodi
E34.1 nawlavuri hormonebis sxva saxis hipersekreciaE34.2 hormonis eqtopiuri sekrecia, romelic ar aris Setanili sxva klasifikaciebSiE34.3 qondriskacoba, romelic ar aris Setanili sxva klasifikaciebSi
qondriskacoba:
. romelic sxvagvarad ar aris dazustebuli
. konstituciuri
. laronis-tipi
. fsiqosocialuriar igulisxmeba: progeria (E 34.8)
rasel-silveris sindromi (Q 87.1)moklekidurebiani aRnagoba imunodeficitTan erTad (D 82.2)qondriskacoba:
. aqondroplaziuri (Q 77.4)
. hipoqondroplaziuri (Q 77.4). specifikuri dismorfuli sindromebis dros - sindromTa kodi aRiniSneba anbanuriindeqsis mixedviT. alimenturi (E 45). hipofizuri (E 23.0)
. Tirkmlismieri (N 25.0)E34.4 konstituciuri simaRle
konstituciuri gigantizmi
E34.5 androgen-rezistentuli sindromimamakacTa fsevdohermafroditizmi androgenuli rezistentobiT
periferiuli hormonuli receptoris dazianebareifenSteinis sindromi
testikuluri feminizacia (sindromi)
E34.8 sxva dazustebuli endokrinuli moSlilobebijalRuzisebri sxeulis funqciis moSla
progeria
E34.9 endokrinuli moSliloba, dauzustebelimoSliloba:
. endokrinuli, romelic sxvagvarad ar aris dazustebuli
. hormonuli, romelic sxvagvarad ar aris dazustebuli
endokrinuli jirkvlebis dazianebebi im avadmyofobebis dros, romlebic
Setanilia sxva klasifikaciebSi
EE35.0* farisebri jirkvlis dazianebebi im avadmyofobTa dros, romlebic
Setanilia sxva klasifikaciebSifarisebri jirkvlis tuberkulozi (A 18.8+)
E35.1* Tirkmelzeda jirkvlis dazianebebi im avadmyofobaTa dros, romlebicSetanilia sxva klasifikaciebSituberkulozuri adisonis avadmyofoba (A 18.7+)vaterhauz-frideriksenis sindromi (meningokokuri) (A 39.1+)
E35.8* sxva endokrinul jirkvlebis dazianebani im avadmyofobTa dros, romlebicSetanilia sxva klasifikaciebSi
E34
E35*
197
endokrinuli sistemis, kvebisa da nivTierebaTa cvlis darRveviT gamowveuli avadmyofobani
sakvebis arasakmao raodenobiT miReba
(E40-E46)
SeniSvna:malnutriciis xarisxi Cveulebriv ganisazRvreba wonis mixedviT da gamoixateba SesabamisiSesaswavli mosaxleobis wonis saSualo sididis normidan gadaxris standartulimaCvenebliT. roca winaswar Catarebulia erTze meti gamokvleva, wonis matebis CamorCenabavSvebSi an bavSvebisa da mozrdilebis wonaSi dakleba, Cveulebriv, sakvebis arasakmarisadmiRebis maCvenebelia. Tu wonaze dakvirveba mxolod erTxel iqna nawarmoebi, diagnozisavaraudoa da ar iTvleba sabolood dadgenilad sxva klinikuri an laboratoriulimonacemebis gareSe. gamonaklis SemTxvevebSi, roca awonva ver xerxdeba, unda daveyrdnoTklinikur dakvirvebas. im SemTxvevebSi, Tu individuumis wonis maCvenebeli mocemulimosaxleobis wonis saSualo sidideze dabalia: mZime malnutricias varaudoben rocawonis normidan qvemoT gadaxra tolia an aRemateba 3 standartul maCvenebels.mosaxleobis wonis saSualo maCvenebelTan SedarebiT: zomier malnutricias varaudoben,roca wonis normidan qvemoT gadaxra aRemateba 2-s da naklebia 3 standartul maCvenebelze;msubuq malnutriciaze msjeloben, roca normidan qvemoT gadaxra aRemateba 1-s, magramnaklebia 2 standartul maCvenebelze.
ar igulisxmeba:nawlavuri malabsorbcia (K 90.-)alimenturi anemiebi (D 50-D 53)cila-energetikuli deficitis Sedegebi (E 64.0)sigamxdre (B 22.2)SimSili (starvacia)(T 73.0)
E kvaSiorkori
mZime malnutricia alimenturi SeSupebiT kanisa da Tmebis pigmentaciis moSlasTan erTad
ar igulisxmeba: marazmuli kvaSiorkori (E 42)E
alimenturi marazmi
mZime malnutricia marazmiT
ar igulisxmeba: marazmuli kvaSiorkori (E 42)E
marazmuli kvaSiorkori
mZime cila-energetikuli malnutricia (rogorc E 43). gardamavali forma
. kvaSiorkorisa da marazmis niSnebiT
E mZime cila-energetikuli deficiti
wonaSi didi raodenobiT dakleba [ganleva] bavSvebsa da mozrdilebSi, an wonaSi matebisCamorCena bavSvebSi, romlis Sedegad miRebuli wonis maCvenebeli sul mcire, 3 erTeuliTCamorCena Sesabamisi mosaxleobis wonis saSualo maCvenebels (an wonaSi msgavsi daklebaaRiniSneba sxva statistikuri gamokvlevebis drosac). Tu Catarebulia mxolod erTidakvirveba, mZime ganlevas varaudoben maSin, roca miRebuli wonis maCvenebeli 3 da metierTeuliT CamorCeba Sesabamisi mosaxleobis wonis saSualo sidides.
starvaciuli SeSupeba
Ezomieri da msubuqi xarisxis cila-energetikuli deficiti
EE44.0 zomieri cila-energetikuli malnutricia
wonis kargva bavSvebsa da mozrdilebSi; an wonaSi matebis CamorCena bavSvebSi, romlisSedegad miRebuli wonis maCvenebeli 2 an meti, magram 3-ze naklebi erTeuliT CamorCenaSesabamisi mosaxleobis wonis saSualo maCvenebels (an wonaSi msgavsi dakleba aRiniSnebasxva statistikuri gamokvlevebis drosac). Tu Catarebulia mxolod erTi dakvirveba,zomier cila-energetikul malnutricias varaudoben maSin, roca miRebuli wonis
E40
E41
E42
E43
E44
198
avadmyofobaTa saerTaSoriso klasifikacia
maCvenebeli 2 an meti, magram 3-ze naklebi erTeuliT CamorCeba Sesabamisi mosaxleobis
wonis saSualo sidides.
E44.1 msubuqi cila-energetikuli malnutriciawonis kargva bavSvebsa da mozrdilebSi an wonaSi matebis CamorCena bavSvebSi, romlisSedegad miRebuli wonis maCvenebeli 1 an meti, magram 2-ze naklebi erTeuliT CamorCebaSesabamisi mosaxleobis wonis saSualo maCvenebels (an wonaSi msgavsi dakleba aRiniSnebasxva statistikuri gamokvlevebis drosac). Tu Catarebulia mxolod erTi dakvirveba,msubuq cila-energetikul malnutricias varaudoben maSin, roca miRebuli wonismaCvenebeli 1 an meti, magram 2-ze naklebi erTeuliT CamorCeba Sesabamisi mosaxleobis
wonis saSualo sidides.
zrda-ganviTarebaSi CamorCena, gamowveuli cila-energetikuli deficitiT
alimenturi:
. qondriskacoba
. zrdis SeCerebafizikuri ganviTarebis Seferxeba, gapirobebuli sakvebis arasakmao raodenobis miRebiT
(malnutriciiT)
E dauzustebeli cila-energetikuli deficiti
SimSiloba, romelic sxvagvarad ar aris dazustebuli
cila-energetikuli disbalansi, romelic sxvagvarad ar aris dazustebuli
kvebiTi deficitis sxva saxeebi
(E50-E64)ar igulisxmeba: alimenturi anemiebi (D 50-D 53)E
A vitaminis deficitiar igulisxmeba: vitamin A deficitis Sedegebi (E 64.1)
E50.0 vitamin A deficiti koniunqtivis qseroziT (simSraliT)E50.1 vitamin A deficiti bitotis laqiTa da koniunqtivis qseroziT (simSraliT)
bitotis laqa mcirewlovan bavSvebSi
E50.2 vitamin A deficiti rqovanas qseroziT (simSraliT)E50.3 vitamin A deficiti rqovanas dawylulebiTa da qseroziT (simSraliT)E50.4 vitamin A deficiti keratomalaciiTE50.5 vitamin A deficiti Ramis sibrmaviTE50.6 vitamin A deficiti rqovanas qserofTalmuri nawiburebiTE50.7 vitamin A deficitis sxva gamovlinebebiT Tvalis mxriv
qserofTalmia, romelic sxvagvarad ar aris dazustebuli
E50.8 vitamin A deficitis sxva gamovlinebebifolikuluri keratozi
qseroderma
E50.9 vitamin A deficiti, dauzustebulihipovitaminozi A, romelic sxvagvarad ar aris dazustebuli
Tiaminis deficiti
ar igulisxmeba: Tiaminis deficitis Sedegebi (E 64.8)E51.1 beri-beri
beri-beri:
E45
E46
E50
E51
199
endokrinuli sistemis, kvebisa da nivTierebaTa cvlis darRveviT gamowveuli avadmyofobani
. mSrali
. sveli + (I 98.8*)
E51.2 vernikes encefalopaTiaE51.8 Tiaminis deficitis sxva gamovlinebebiE51.9 Tiaminis deficiti, dauzustebeliE
nikotinmJavas deficiti [pelagra]
deficiti:. niacin (- triftofanis). nikotinamidispelagra (alkoholuri)ar igulisxmeba: niacinis deficitis Sedegebi (E 64.8)
E
B jgufis sxva vitaminebis deficitiar igulisxmeba: vitamin B deficitis Sedegebi (E 64.8)
vitamin B12 deficituri anemia (D 51.-)E53.0 riboflavinis deficiti
ariboflavinozi
E53.1 piridoqsinis deficitivitimin B6
deficiti
ar igulisxmeba: piridoqsin damokidebuli sideroblasturi anemia (D 64.3)E53.8 B B jgufis vitiminebis sxva dazustebuli saxis deficiti
deficiti:
. biotinis
. ciankobalaminis
. folatis
. foliumis mJavis
. panTotenis mJavis
. vitamin B12-isE53.9 vitamin B deficiti, dauzustebeli
askorbinis mJavis deficiti
vitamin C deficiti
skorbuti [suravandi]ar igulisxmeba: skorbutuli anemia (D 53.2)
vitamin C deficitis Sedegebi (E 64.2)E
D vitaminis deficitiar igulisxmeba: mozrdilTa osteomalacia (M 83.-)osteoporozi (M 80-M 81)raqitis Sedegebi (E 64.3)
E55.0 raqiti, aqtiuriosteomalacia:
. bavSvTa
. mozardTaar igulisxmeba: raqiti:
. celiakuri (K 90.0)
. kronis (K 50.-)
. araaqtiuri (E 64.3)
. Tirkmlismieri (N 25.0)
. vitamin-D-rezistentuli (E 83.3)
E55
E54
E52
E53
200
avadmyofobaTa saerTaSoriso klasifikacia
E55.9 vitamin D-s deficiti, dauzustebeliavitaminozi D
Esxva vitaminebis deficiti
ar igulisxmeba:sxva vitaminebis deficitis Sedegebi (E 64.8)E56.0 vitamin E-s deficitiE56.1 vitamin K-s deficiti
ar igulisxmeba:vitamin K-s deficitiT gamowveuli koagulaciuri faqtoris deficiti (D 68.4)axalSobilTa vitamin K-s deficiti (P 53)
E56.8 sxva vitaminebis deficitiE56.9 vitaminis deficiti, dauzustebeli
E sakvebSi kalciumis deficiti
ar igulisxmeba: kalciumis cvlis darRvevebi (E 83.5)kalciumis deficitis Sedegebi (E 64.8)
sakvebSi seleniumis deficiti
keSanis avadmyofoba
ar igulisxmeba: seleniumis deficitis Sedegebi (E 64.8)E
sakvebSi TuTiis deficiti
E
sxva sakvebi elementebis deficiti
Tu wamlismieria da wamlis identifikacia gsurT, gamoiyeneT damatebiTi gare mizezebiskodi (Tavi XX)ar igulisxmeba: mineraluri cvlis darRvevebi (E 83.-) iodis deficitTan dakavSirebuli
farisebri jirkvlis avadmyofobebi (E00-E02) malnutriciis da sxva kvebiTi deficitis Sedegebi (E 64.-)
E61.0 spilenZis deficitiE61.1 rkinis deficiti
ar igulisxmeba: rkina-deficituri anemia (D 50.-)E61.2 magniumis deficitiE61.3 manganumis deficitiE61.4 qromis deficitiE61.5 molibdenis deficitiE61.6 vanadiumis deficitiE61.7 ramdenime sakvebi elementis erTdrouli deficitiE61.8 sxva dazustebuli sakvebi elementis deficitiE61.9 sakvebi elementis deficiti, dauzustebeli
sxva kvebiTi deficiti
ar igulisxmeba: dehidracia (E 86)zrdaSi CamorCena (R 62.8)axalSobilTa kvebis problemebi (P 92.-)malnutriciis da sxva kvebiTi deficitis Sedegebi (E64.-)
E63.0 esenciuri cximovani mJavebis deficitiE63.1 miRebuli sakvebis Semadgeneli nawilebis balansis darRvevaE63.8 sxva dazustebuli kvebiTi deficitebi
E56
E58
E59
E60
E61
E63
201
endokrinuli sistemis, kvebisa da nivTierebaTa cvlis darRveviT gamowveuli avadmyofobani
E63.9 sakvebis deficiti, dauzustebelialimenturi kardiomiopaTia, romelic sxvagvarad ar aris dazustebuli (I 43.2*)
Ekvebis deficitisa da sxva sakvebi elementebis deficitis Sedegebi
EE64.0 cila-energetikuli deficitis Sedegebi
ar igulisxmeba:zrda-ganviTarebis Seneleba, gamowveuli cila-energetikuli deficitiT (E45)E64.1 vitamin A deficitis SedegebiE64.2 vitimin C deficitis SedegebiE64.3 raqitis SedegebiE64.8 sakvebis naklebobis sxva SedegebiE64.9 sakvebis dauzustebeli deficitis Sedegebi
simsuqne da Warbi kvebis saxeebi
(E65-E68)E
adgilobrivi simsuqne
cximovani baliSi
E simsuqne
ar igulisxmeba: adipozo-genitaluri distrofia (E 23.6)lipomatozi:. romelic sxvagvarad ar aris dazustebuli (E 88.2). mtkivneuli (dolorosa) [derkumis] (E 88.2)prader-vilis sindromi (Q 87.1)
E66.0 Warbi kaloriebis Sedegad ganviTarebuli simsuqneE66.1 wamliT-gamowveuli simsuqne
Tu wamlis identifikacia gsurT, gamoiyeneT damatebiTi gare mizezebis kodi (Tavi XX)
E66.2 ukiduresi simsuqne alveoluri hipoventilaciiTpikvikis sindromi
E66.8 sxva saxis simsuqneavadmyofuri simsuqne
E66.9 simsuqne, dauzustebelimartivi simsuqne, romelic sxvagvarad ar aris dazustebuli
E
Warbi kvebis sxva saxeebi
ar igulisxmeba:hiperalimentacia, romelic sxvagvarad ar aris dazustebuli (R 63.2)hiperalimentaciis Sedegebi (E 68)
E67.0 hipervitaminozi AE67.1 hiperkarotinemiaE67.2 megavitamin-B6
sindromiE67.3 hipervitaminozi DE67.8 sxva dazustebuli hiperalimentaciebiE
hiperalimentaciis Sedegebi
E64
E65
E66
E67
E68
202
avadmyofobaTa saerTaSoriso klasifikacia
metaboluri darRvevebi
(E70-E90)
ar igulisxmeba: androgen-rezistentuli sindromi (E 34.5)Tirkmelzeda jirkvlis Tandayolili hiperplazia (E 25.0)elers-danlosis sindromi (Q 79.6)fermentuli moSlilobebiT gapirobebuli hemolizuri anemiebi (D 55.-)marfanis sindromi (Q 87.4)5-a- reduqtazis deficiti (E 29.1)
aromatuli aminomJavebis metabolizmis darRvevebi
EE70.0 klasikuri fenilketonuriaE70.1 sxva hiperfenilalaninemiebiE70.2 Tirozinis metabolizmis darRvevebi
alkaptonuria
hiperTirozinemiaoqronoziTirozinemia
Tirozinozi
E70.3 albinizmialbinizmi:
. okuluri
. okulokutaneuri (Tval-kanis)sindromi:. Cediak (-Steinbrinq)-higaSis. krosis
. helmanski-pudlekis
E70.8 aromatuli aminomJavebis metabolizmis sxva darRvevebidarRveva:
. histidinis metabolizmis
. triftofanis metabolizmis
E70.9 aromatuli aminomJavis metabolizmis darRveva, dauzustebeli
ganStoebuljaWviani aminomJavebisa da cximovani mJavebis metabolizmis
darRvevebi
EE71.0 nekerCxlis sirofis msgavsi Sardis avadmyofobaE71.1 ganStoebuljaWviani aminomJavebis metabolizmis sxva darRvevebi
hiperleicin-izoleicinemia
hipervalinemiaizovalerianis acidemiameTilmalonis acidemia
propionis acidemia
E71.2 ganStoebuljaWviani aminomJavis metabolizmis darRveva, dauzustebeliE71.3 cximovani mJavebis metabolizmis darRvevebi
adrenoleikodistrofia [adison-Silderis]
kunTovani karnitinpalmitiltransferazis deficitiar igulisxmeba: revsamis avadmyofoba (G 60.1)
Silderis avadmyofoba (G 37.0)cilvegeris sindromi (Q 87.8)
E70
E71
203
endokrinuli sistemis, kvebisa da nivTierebaTa cvlis darRveviT gamowveuli avadmyofobani
aminomJavebis metabolizmis sxva darRvevebi
ar igulisxmeba:normidan gadaxrili monacemebi avadmyofobis gamovlinebis gareSe (R70-R89)
darRvevebi:. aromatuli aminomJavebis metabolizmis (E 70.-)
. . ganStoebuljaWviani aminomJavebis metabolizmis (E71.0-E71.2). cximovani mJavebis metabolizmis (E 71.3). purinisa da pirimidinis metabolizmis (E79.-)nikrisi (M 10.-)
E72.0 aminomJavebis transportis darRvevebicistinozi
cistinuriafankoni (-de toni) (-debres) sindromihartnafis avadmyofobaloves sindromi
ar igulisxmeba: triftofanis metabolizmis darRvevebi (E 70.8)E72.1 gogirdSemcveli aminomJavebis metabolizmis darRvevebi
cistaTioninuria
homocistinuriameTioninemiasulfitoqsidazis deficiti
ar igulisxmeba: transkobalamin II deficiti (D 51.2)E72.2 Sardovanas ciklis metabolizmis darRvevebi
argininemia
argininosukcinuri aciduriacitrulinemiahiperamonemia
ar igulisxmeba:ornitinis metabolizmis darRvevebi (E 72.4)E72.3 lizinisa da hidroqsilizinis metabolizmis darRvevebi
glutaris aciduria
hidroqsilizinemia
hiperlizinemia
E72.4 ornitinis metabolizmis darRvevebiirnitinemia (tipi I, II)
E72.5 glicinis metabolizmis darRvevebihiperhidroqsiprolinemia
hiperprolinemia (tipi I, II)ara-ketonuri hiperglicinemia
sarkozinemia
E72.8 aminomJavebis metabolizmis sxva dadgenili darRvevebidarRvevebSi:
. bB-aminomJavis metabolizmis
. g-glutamilis ciklis
E72.9 aminomJavebis metabolizmis moSla, dauzustebeli
E laqtozis autanloba
E73.0 laqtozis Tandayolili deficitiE73.1 laqtozis meoradi deficitiE73.8 laqtozis sxva saxis autanlobaE73.9 laqtozis dauzustebeli autanloba
E72
E73
204
avadmyofobaTa saerTaSoriso klasifikacia
E naxSirwylebis metabolizmis sxva darRvevebi
ar igulisxmeba: glukagonis gazrdili sekrecia (E 16.3)Saqriani diabeti (E 10-E 14)hipoglikemia, romelic sxvagvarad ar aris dazustebuli (E 16.2)mukopolisaqaridozi (E 76.0-E 76.3)
E74.0 glikogenis dagrovebis avadmyofobagulis glikogenozi
avadmyofoba:. andersenis. koris. forbesis. hersis. makardlis. pompes. tauris. fon girkes
. RviZlis fosforilazis deficiti
E74.1 fruqtozis metabolizmis darRvevebiesenciuri fruqtozuria
fruqtozo-1,6-difosfatazis deficiti
fruqtozis memkvidruli autanloba
E74.2 galaqtozis metabolizmis darRvevebigalaqtokinazis deficiti
galaqtozemia
E74.3 nawlavebSi naxSirwylebis Sewovis sxva darRvevebSiglukoza-galaqtozis malabsorbcia
saqarozis ukmarisoba
ar igulisxmeba: laqtozis autanloba (E 73.-)E74.4 piruvatis metabolizmis da glukoneogenezis darRvevebi
deficiti:
. fosfoenolpiruvatkarboqsikinazis
. piruvatis
. karboqsilazis
. dehidrogenazis
ar igulisxmeba: anemiasTan erTad (D 55-)E74.5 naxSirwylebis metabolizmis sxva specifiuri darRvevebi
esenciuri pentozuria
oqsalozioqsaluria
Tirkmlismieri glukozuria
E74.9 naxSirwylebis metabolizmis darRveva, dauzustebeli
sfingolipidebis metabolizmis darRvevebi da lipidebis dagrovebis sxva
darRvevebi
ar igulisxmeba: mukolipidozi, tipi III (E 77.0-E 77.1)revsamis avadmyofoba (E 60.1)
E75.0 GM2 gangliozidoziavadmyofoba:
. sandhofis
. Tei-saqsisGM2 ganliozidozi:
E71E74
E75
205
endokrinuli sistemis, kvebisa da nivTierebaTa cvlis darRveviT gamowveuli avadmyofobani
.Nromelic sxvagvarad ar aris dazustebuli
. mozrdilTa
. mozardTa
E75.1 sxva gangliozidozebigangliozidozi:
. romelic sxvagvarad ar aris dazustebuli
. GM1
. GM3
mukolipidozi IV
E75.2 sxva sfingolipidozebiavadmyofoba:
. fabris (-andersonis)
. goSes
. krabes
. niman-pikisfarberis sindromimetaqromuli leikodistrofiasulfatazis deficiti
ar igulisxmeba: adrenoleikodistrofia (adison-Silderis) (E 71.3)E75.3 sfingolipidozi, dauzustebeliE75.4 neironuli ceroiduli lipofuscinozi
avadmyofoba:
. batenis
. bilSovski-ianskis
. kafis
. Spilmeier-vogtis
E75.5 sxva lipidebis dagrovebiT mimdinare avadmyofobebicerebrotendinuri qolesterozi (van bogart-Serer-ebSteinis)
volmanis avadmyofoba
E75.6 lipidebis dagrovebis darRvevebi, dauzustebeli
glikozaminoglikanebis darRvevebi, dauzustebeli
E
E76.0 mukopolisaqaridozi, tipi Isindromi:
. harleris
. harker-Seies
. Seies
E76.1 mukopolisaqaridozi, tipi IIhanteris sindromi
E76.2 sxva mukopolisaqaridozebib-glukuronidazis deficiti
mukopolisaqaridozi, tipi III,IV,VI,VIIsindromi:. maroto-lamis (msubuqi) (mZime). morkuios (-msgavsi) (klasikuri)
. sanfilipos (tipi B)(tipi C)(tipi D)E76.3 mukopolisaqaridozi, dauzustebeliE76.8 glikozaminoglikanebis metabolizmis sxva darRvevebiE76.9 glikozaminoglikanis metabolizmis darRveva, dauzustebeliE
E76
206
avadmyofobaTa saerTaSoriso klasifikacia
glikoproteinebis metabolizmis darRvevebi
E77.0 lizosomuri fermentebis posttranslaciuri modifikaciis defeqtebimukolipidozi II (I-ujredis avadmyofoba)
mukolipidozis III (fsevdo-harleris polidistrofia)
E77.1 glikoproteinis daSlis defeqtebiaspartilglukozaminuria
fukozidozimanozidozi
sialidozi (mukolipidozi I)
E77.8 glikoproteinebis metabolizmis sxva darRvevebiE77.9 glikoproteinis metabolizmis darRveva, dauzustebeli
E lipoproteinebis metabolizmis darRvevebi da sxva lipidemiebi
ar igulisxmeba: sfingolipidozi (E 75.0-E 75.3)E78.0 WeSmariti hiperqolesterinemia
ojaxuri hiperqolesterinemia
fredriqsonis hiperlipoproteinemia, tipi IIaühiper -b-lipoproteinemiahiperlipidemia, jgufi Adabali simkvrivis lipoproteinuli tipis (LDL) hiperlipoproteinemia
E78.1 WeSmariti hipergliceridemiaendogenuri hipergliceridemia
fredriqsonis hiperlipoproteinemia, tipi IVhipirlipidemia, jgufi Bhiperpre -b-lipoproteinemiaZalian dabali simkvrivis lipoproteinuli tipis (VLDL)hiperlipoproteinemia
E78.2 Sereuli hiperlipidemiafarTe anu flotirebuli b- lipoproteinemia
fredriqsonis hiperlipoproteinemia, tipi IIbü an IIIhiper-b-lipoproteinemia pre-b-lipoproteinemiiThiperqolesterinemia endogenuri hipergliceridemiiThiperlipidemia, jgufi Ctubero-eruptiuli tipis qsanTomatuberozuli qsanToma (Xanthoma tuberosum)ar igulisxmeba: cerebrotendinuri qolesterozi (van bogart-Serer-epSteinis) (E 75.5)
E78.3 hiperqilomikronemiafredriqsonis hiperlipoproteinemia, tipi I an V
hiperlipidemia, jgufi DSereuli hipergliceridemia
E78.4 sxva hiperlipidemiebiojaxuri kombinirebuli hiperlipidemia
E78.5 hiperlipidemia, dauzustebeliE78.6 lipoproteinTa deficiti
a-b-lipoproteinemia
maRali-simkvrivis lipoproteinTa deficitihipo-a-lipoproteinemiahipo-b-lipoproteinemia (ojaxuri)
lecitinqolesterolaciltransferazis deficiti
teinjeris avadmyofoba
E77
E78
207
endokrinuli sistemis, kvebisa da nivTierebaTa cvlis darRveviT gamowveuli avadmyofobani
E78.8 lipoproteinebis metabolizmis sxva darRvevebiE78.9 lipoproteinebis metabolizmis moSla, dauzustebeli
E purinebis da pirimidinebis metabolizmis darRvevebi
ar igulisxmeba: Tirkmlis kenWi (N 20,0)kombinirebuli imunodeficituri darRvevebi (D 81.-)nikrisi (podagra) ( M 10.-)orotaciduriuli anemia (D 53.0)pigmenturi qseroderma (Q 82.1)
E79.0 hiperurikemia anTebiTi arTritisa da podagruli avadmyofobis niSnebisgareSeasimptomuri hiperurikemia
E79.1 leS-nihenis sindromiE79.8 purinisa da pirimidinis metabolizmis sxva darRvevebi
memkvidruli qsanTinuria
Eporfirinebisa da bilirubinis metabolizmis darRvevebi
igulisxmeba:katalazis da peroqsidazis defeqtebi
E80.0 memkvidruli eriTropoezuri porfiriaTandayolili eriTropoezuri porfiria
eriTropoezuri protoporfiria
E80.1 kanis gviani porfiriaE80.2 sxva saxis porfiria
memkvidruli koproporfiria
porfiria:.Nromelic sxvagvarad ar aris dazustebuli. mwvave xangamoSvebiTi (RviZlis)
Tu mizezis identifikacia gsurT, isargebleT damatebiT gare mizezTa kodiT (Tavi XX)
E80.3 katalazis da peroqsidazis defeqtebiakatalazia (takapara)
E80.4 jilbertis sindromiE80.5 krigler-najaris sindromiE80.6 bilirubinis metabolizmis sxva darRvevebi
dubin-jonsonis sindromi
rotorsis sindromi
E80 .7 bilirubinis metabolizmis moSla, dauzustebeliE
mineraluri cvlis darRvevebi
ar igulisxmeba: sakvebi mineralebis deficiti (E 58-E 61)farisebralo jirkvlis avadmyofobebi (E 20-E 21)vitamin D-s deficiti (E 55.-)
E83.0 spilenZis metabolizmis darRvevebimenkes (xveuli Tmis) (foladisebri Tmis) avadmyofoba
vilsonis avadmyofoba
E83.1 rkinis metabolizmis darRvevebihemoqromatozi
ar igulisxmeba: .anemia:. rkinadeficituri (D 50.-). sideroblasturi (D 64.0-D 64.3)
E79
E83
E80
208
avadmyofobaTa saerTaSoriso klasifikacia
E83.2 TuTiis metabolizmis darRvevebieteropaTiuli akrodermatiti
E83.3 fosforis metabolizmis darRvevebimJave fosfatazis deficiti
ojaxuri hipofosfatemiahipofosfataziavitamin - D -rezistenuli:. osteomalacia. raqiti
ar igulisxmeba: mozrdilTa osteomalacia (M 83.-)osteoporozi (M 80.-M 81)
E83.4 magniumis metabolizmis darRvevebihipermagniemia
hipomagniemia
E83.5 kalciumis metabolizmis darRvevebiojaxuri hipokalciuriuli piperkalciemia
idiopaTiuri piperkalcinozi
ar igulisxmeba: qondrokalcinozi (M 11.1-M 11.2)hiperparaTiroidizmi (E 21.0 -E 21.3)
E83.8 mineraluri metabolizmis sxva darRvevebiE83.9 mineralTa metabolizmis darRvevebi, dauzustebeliE
cisturi fibrozi
igulisxmeba: mukoviscidozi
E84.0 cisturi fibrozi pulmonuri gamovlinebebiTE84.1 cisturi fibrozi nawlavuri gamovlinebebiTE84.8 cisturi fibrozi sxva gamovlinebebiT
cisturi fibrozi kombinirebuli gamovlinebebiT
E84.9 cisturi fibrozi dauzustebeli
amiloidozi
ar igulisxmeba: alchaimeris avadmyofoba (G 30.-)E85.0 araneiropaTiuli memkvidruli ojaxuri amiloidozi
xmelTaSuazRvispiruli ojaxuri cxeleba
memkvidruli amiloiduri nefropaTia
E85.1 neiropaTiuli memkvidruli ojaxuri amiloidoziamiloiduri polinevropaTia (portugaliuri)
E85.2 memkvidruli ojaxuri amiloidozi dauzustebeliE85.3 meoradi sistemuri amiloidozi
hemodializTan dakavSirebuli amiloidozi
E85.4 gansazRvrul organoSi ganviTarebuli amiloidozilokalizebuli amiloidozi
E85.8 sxva amiloidozebiE85.9 amiloidozi daudgeneli
E moculobis Semcireba
dehidracia
sisxlis plazmis moculobis an ujredSorisi siTxis moculobis Semcirebahipovolemia
E86
D84
E85
209
endokrinuli sistemis, kvebisa da nivTierebaTa cvlis darRveviT gamowveuli avadmyofobani
ar igulisxmeba: axalSobilTa dehidracia (P 74.1)hipovolemiuri Soki:. romelic sxvagvard ar aris dazustebuli (R 57-1). postoperaciuli (T 81.1). travmuli (T 79.4)
siTxeebis, eleqtrolitebis da mJava-tutovani wonasworobis sxva
darRvevebi
E87.0 hiperosmolaroba da hipernatriemiaNa-is siWarbe
Na-iT gadatvirTva
E87.1 hipoosmolaroba da hiponatriemiaNa-is deficitiar igulisxmeba: antidiurezuli hormonis Seusabamo sekreciis sindromi (E 22.2)
E87.2 acidoziacidozi:.Nromelic sxvagvarad ra aris dazustebuli. rZis mJavis. metaboluri. respiraciuli
ar igulisxmeba: diabeturi acidozi (E 10-E 14 saerTo meoTxe rigiT.1)
E87.3 alkalozialkalozi.Nromelic sxvagvarad ar aris dazustebuli. metaboluri
. respiraciuli
E87.4 mJava-tutovani wonasworobis Sereuli darRvevebiE87.5 hiperkaliemia
K-is siWarbe
K-iT gadatvirTva
E87.6 hipokalemiaK-is deficiti
E87 .7 qsovilovani siTxis siWarbear igulisxmeba: SeSupeba (R 60.-)
E87.8 siTxisa da eleqtrolitTa balansis sxva darRvevebi romlebic ar arisSetanili sxva klasifikaciebSieleqtrolituri disbalansi, romelic sxvagvarad ar aris dazustebuliNOhiperqloremia
hipoqloremia
sxva metaboluri darRvevebi
ar igulisxmeba: histiocitozi X (qronikuli) (D 76.0)Tu wamlismieria da wamlis identifikacia gsurT, isargebleT damatebiT
gare mizezTa kodiT (Tavi XX)
E88.0 sisxlis plazmis cilebis metabolizmis, darRvevebi, romelic ar arisSetanili sxva klasifikaciebSia-1-antitrifsinis deficitibis-albuminemiaar igulisxmeba: lipoproteinebis metabolizmis moSla (E 78.-)
E87
E88
210
avadmyofobaTa saerTaSoriso klasifikacia
monoklonuri gamapaTia (D 47.2)poliklonuri hipergamaglobulinemia (D 89.0)valdenStromis makroglobulinemia (C 88.0)
E88.1 lipodistrofia, romelic ar aris Setanili sxva klasifikaciebSilipodistrofia, romelic sxvagvarad ar aris dazustebuli
ar igulisxmeba: uiplis avadmyofoba (K 90.8)E88.2 lipomatozi, romelic ar aris Setanili sxva klasifikaciebSi
lipomatozi.Nromelic sxvagvarad ar aris dazustebuli
. mtkivneuli (dolorosa) (derkumis)
E88.8 sxva dadgenili metaboluri darRvevebibensaudis adenolipomatozi - lavnua
trimeTilaminuria
E88.9 metaboluri darRveva daudgeneli
procedurebis Semdgomi endokrinuli da metaboluri darRvevbi, romlebic
ar aris Setanili sxva klasifikaciebSi
E89.0 postproceduruli hipoTiroidizmipostiradiaciuli hipoTiroidizmi
postoperaciuli hipoTiroidizmi
E89.1 postproceduruli hipoinsulinemiapankreasis amokveTis Semdgomi hiperglikemia
E89.2 postproceduruli hipoparaTiroidizmifarisebraxlo jirkvlis ararsebobiT gamowveuli tetania
E89.3 postproceduruli hipopituitarizmipostiradiaciuli hipopituitarizmi
E89.4 sakvercxis postproceduruli ukmarisobaE89.5 saTesle jirkvlebis postproceduruli hipofunqciaE89.6 Tirkmelzeda jirkvlis (tvinovani Sris) postprceduruli hipofunqciaE89.8 sxva postproceduruli endokrinuli da metaboluri darRvevebiE89.9 postproceduruli da metaboluri darRvevebi, daudgeneli
alimenturi da metaboluri darRvevebi im avadmyofobebis dros, romlebic
Setanilia sxva klasifikaciebSi
E90*
E89