Diagnostic Diferential Hepatosplenomegalie
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Transcript of Diagnostic Diferential Hepatosplenomegalie
Diagnostic diferential hepatomegalie:
Diagnostic diferential al hepatomegaliei:cresterea in dimensiuni a ficatului
Inflamatie:
hepatita
hepatita infectioasa:
hepatita virala
schistosomiaza
hepatita alcoolica
hepatita toxica
hepatita indusa de medicamente
autoimun
abces hepatic
piogen
amoebic
colangita
pericolangita
alte infectii
mononucleoza infectioasa
tuberculoza miliara
leishmania donovani
amoebiaza
Ciroza
ciroza alcoolica
posthepatita
postnecrotic
ciroza biliara
hemocromatoza cu ciroza
Neoplasm malign: carcinom hepatocelular
colangiocarcinom
angiosarcom
metastaze:
carcinom de pancreas
carcinom de colon
carcinom pulmonar
carcinom mamar
carcinom de stomac
Neoplasm benign: adenom hepatic
hemangiom
hiperplazie nodulara focala
Hematologie, limfoproliferativ:
limfom
leucemie
mielofibroza cu metaplazie mieloida
mielom multiplu
Granulomatos:
sarcoidoza
tuberculoza miliara
Metabolic:
hemocromatoza
deficienta de alfa 1 antitripsina
boala Wilson
fibroza chistica
Kwashiorkor(deficienta alimentara de proteine)
Obstructie biliara
coledocolitiaza
pancreatita
strictura biliara
carcinom
compresie externa
Congestie hepatica:
ICC
Pericardita constrictiva
Sdr Budd Chiari
Tromboza
Tumora
Retea in vena cava inferioara
Tulburari infiltrative de depozitare
infiltrare grasa alcoolica
boala de depozitare a lipidelor
boala Gaucher
boala Niemann-Pick
ficatul gras
boala depozitarii de glicogen
amiloidoza
boala Wilson
sindromul Hurler
Altele:
chisturi
boala hidatica a ficatului.
Diagnostic diferential al hepatosplenomegaliei:cresterea in dimensiuni a ficatului si splinei.
Hipertensiunea portala:
ciroza
sdr Budd Chiari (stenoza sau ocluzia venei hepatice)
Boala Banti (hipertensiune portala idiopatica)
Sarcoidoza
Ciroza biliara primara
Ficat chistic
Metastaze hepatice multiple
Ficat congestionat
Ficat gras
Colestaza extrahepatica
Tumori
Inhibitori ai anhidrazei carbonice
Calculi
Icter medicamentos
Infectii
hepatita virala
bruceloza (boala Bang)
mononuceloza infectioasa
febra tifoida abdominala
amebiaza
malarie
leptospiroza
febra recurenta
echinococoza
schistosomiaza
leishmaniaza
histplasmoza
bilaharzioza
Reticuloze
boala Letterer- Siwe(reticuloza la copii si adolescenti)
Hematologic, mieloproliferativ
Trombocitopenie idiopatica
Policitemie
Osteomieloscleroza
Mieloza cronica
Limfom Hodgkin Leucemie
Anemie hemolitica/hemoglobinopatii:
talasemie anemie falciforma
deficienta de glucoza 6-fosfat
anemie imun-hemoliticaTulburari metabolice:
boala Gaucher
boala Wilson
boala Niemann-Pick
hemocromatoza
galactozemie
amiloidoza
sindromul Pfaundler-Hurler
glicogenoza tip IV
hiperlipemie familiala
Altele
fibroza chistca
histiocitoza X
sindromul Felty(splenomegalie cu artrita reumatoida si leucopenie)
Morbus haemolyticus neonatorum
Boala Still(artrita reumatoida juvenila)
Boala Osler
Anemia sideroblastica
Microangiopatia Moschcowitz
Tuberculoza miliara
Embolii pulmonare recurente