Post on 16-Jan-2016
description
(Myasthenia Gravis)
-,,,
- 1 2 3 Schwanns 4 -
--
-
-
nAchR
-
-104-204/m2
-4
2(42kD),(56kD),(66kD),(80kD)
-2
-
AATP., ..
nAchR (nAchR-Ab),, 50-60: 60: 73:(nAchR),
T *80% *33%-75% *nAchRT
*20-30 40-50* : = 1 : 1.5*-,,; ,,-****
Osserman. a b
14-18
:: : (ChEI):
1.2.Jollys3.ChEI4.AchR
1. ChEI ChEI ChEI 23.4.
(Eaton -Lambert).: .
(Prostigmine) 15-30mg3-4/ (Pyridostigmine) 60-120 mg; 3-4/ (Methylprednisolone) 0.5-1.0g/3-5 (Azathioprine) 50-100mg/
-
1.
2.
60